Dental Management for Alagille Syndrome: A Case Report

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Published: Jun 27, 2019
Keywords:
Alagille syndrome Dental management Oral manifestations

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Onauma Angwaravong
Department of Preventive Dentistry, Faculty of Dentistry, Khon Kaen University, Amphur Muang, Khon Kaen
Rutchada Kittiprawong
Dental Department, Thabo Crown Prince Hospital, Amphur Thabo, Nong Khai.
Thidarat Angwarawong
Department of Prosthodontics, Faculty of Dentistry, Khon Kaen University, Amphur Muang, Khon Kaen.

Abstract

Alagille syndrome is a complex genetic disorders, having high variability in severity and multi-organ system involvement, with the presence of at least three out of five major systems: liver, heart, skeletal, eye, face, and some other organs may be involved. A multidisciplinary approach is needed to manage Alagille syndrome. Dental management for patient with Alagille syndrome could be different from healthy patients due to multi-organ disorders especially the impairments of liver function and congenital heart defects. Up to date, there are few articles addressing dental management for patients with Alagille syndrome. Thus, this article aims to review literatures related to Alagille syndrome regarding the etiology, incidence, clinical features, diagnosis, treatment, and dental management with case report.

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How to Cite
1.
Angwaravong O, Kittiprawong R, Angwarawong T. Dental Management for Alagille Syndrome: A Case Report. Khon Kaen Dent J [Internet]. 2019 Jun. 27 [cited 2024 Apr. 24];22(1):69-80. Available from: https://he01.tci-thaijo.org/index.php/KDJ/article/view/198593
Issue
Vol. 22 No. 1 (2019)
Section
Clinical Science

บทความ ข้อมูล เนื้อหา รูปภาพ ฯลฯ ที่ได้รับการลงตีพิมพ์ในวิทยาสารทันตแพทยศาสตร์ มหาวิทยาลัยขอนแก่นถือเป็นลิขสิทธิ์เฉพาะของคณะทันตแพทยศาสตร์ มหาวิทยาลัยขอนแก่น หากบุคคลหรือหน่วยงานใดต้องการนำทั้งหมดหรือส่วนหนึ่งส่วนใดไปเผยแพร่ต่อหรือเพื่อกระทำการใด ๆ จะต้องได้รับอนุญาตเป็นลายลักษณ์อักษร จากคณะทันตแพทยศาสตร์ มหาวิทยาลัยขอนแก่นก่อนเท่านั้น

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